Open Access Macedonian Journal of Medical Sciences.
http://dx.doi.org/10.3889/oamjms.2015.036
Case Report
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Klippel Trenaunay Syndrome: A
Case Report in an Adolescent Nigerian Boy
Anthonia Asanye Ikpeme1*, Usang Edet Usang2,
Akan Wilson Inyang2, Nchiewe Ani1
1University of Calabar Teaching Hospital, Radiology, University
of Calabar, PMB 1115, Nigeria; 2University of Calabar Teaching
Hospital, Department of Surgery, University of Calabar, PMB 1115, Nigeria
AIM: This is to report a case of Klippel Trenauay Weber syndrome in a
fifteen year old Nigerian boy. This is a rare syndrome and it is the first
case to be reported in UCTH Calabar.
CASE PRESENTATION: Product of a full term uneventful pregnancy,
delivered to non-consanguineous apparently healthy parents. At birth was
noted to gradually develop swelling on the right leg, worse at the right
foot. There was crossed hemi-hypertrophy with right leg bigger than the
left. As child grew symptoms worsened, parents separated and eventually he
was abandoned to the streets. He presented at University of Calabar Teaching
Hospital for medical care at the age of fifteen years with lymphatic
obstruction, persistent foul smelling drainage, lipodermatosclerosis of
right foot as well psycho-social and financial constraints. The diagnosis
was made with x-rays and Doppler studies of the lower limb vessels. He is
currently being managed conservatively with compression dressings on the
affected limbs, Antibiotics for the infection and analgesics. De-bulking
surgery is being anticipated at this time.
CONCLUSION: This is a case of KTWS presenting in adolescence and due
to its rarity in Nigeria, this report is to increase awareness.
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Citation: Ikpeme AA, Usang UE, Inyang AW, Ani
N. Klippel Trenaunay Syndrome: A Case Report in an Adolescent Nigerian Boy.
OA Maced J Med Sci. http://dx.doi.org/10.3889/oamjms.2015.036
Key words: Klippel-Trenaunay Weber syndrome; Adolescent; Port wine
stain; infection.
*Correspondence: Anthonia Asanye Ikpeme. University of Calabar Teaching
Hospital, Radiology, 4 Elijah Henshaw Street, Calabar, Cross River 54001,
Nigeria. E-mail: ikpemeanthonia@yahoo.com
Received: 18-Nov-2015; Revised: 28-Feb-2015; Accepted: 03-Mar-2015; Online
first: 28-Mar-2015
Copyright: © 2015 Anthonia Asanye Ikpeme, Usang Edet Usang, Akan
Wilson Inyang, Nchiewe Ani. This is an open access article distributed under
the terms of the Creative Commons Attribution License, which permits
unrestricted use, distribution, and reproduction in any medium, provided the
original author and source are credited.
Competing Interests: The authors have declared that no competing
interests exist.
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